Keimyung Medical Journal, Vol.8(1) : 189-193, 1989
Renal angiomyolipomas are uncommon benign neoplasms composed of blood vessels, fat tissues and smooth muscles. The ability to diagnose angiomyolipoma accuarately with radiographic technique has increased greatly. Therefore conservative therapy was recommended. However, hemorrhage into or around the tumor may complicate these appearances by obscuring characteristic feature. Massive retroperitoneal hemorrhagic angiomyolipomas ended up with nephrectomy in most case. We report a case of massive retroperitoneal hemorrhage from spontaneous rupture of a renal angiomyolipoma in 38 years old man. The clinical presentation and management of renal angiomyolipoma are discussed.