순형 폐동맥 폐쇄증 1례

Abstract

Pulmonary atresia with intact ventricular septum is uncommon congenital cardiac anomaly constituting less than 1% of congenital heart disease. Authors experienced a case of pulmonary atresia with intact ventircular septum in a 95 day-old male. Diagnostic confirmation was made by 2-D echocardiography, cardiac catheterization and angiography. Right ventricular outflow reconstruction with Xenomedica, tricupid valve commissurotomy, closure of patent foramen ovale, and concomitant pumonary valvectomy were performed surgically.