미만성 폐 림프관종증의 CT 소견 : 증례보고

Abstract

Diffuse pulmonary lymphangiomatosis(DPL) is a very rare, progressive pulmonary abnormality of lymphatic system that occurs in children and young adults. We presented CT findings of DPL in a young girl, which was characterized by diffuse, smooth thickening of bronchovascular bundles and interlobular septa especially in the subpleural regions of both lower lobes, associated with recurrent pleural effusion. Pathologically, the disorder revealed increased numbers of anastomosing lymphatic channels in the pleura and subpleural interlobular septa.