선천성 회장 폐쇄증이 동반된 담도 폐쇄증 1례

Abstract

Biliary atresia is a progressive obliterative cholangiopathy. However, the actual causes remain unknown, although a number of factors such as developmental malformation, viral infection, toxicity of bile constituents, and anatomic abnormality in the hepatobiliary system have been considered. Recently, several studies have been done to find out specific gene expression. Some cases of biliary atresia are associated with anomalies of cardiovascular system, digestive tract and spleen. Few cases of biliary atresia with congenital ileal atresia were reported. We experienced a case with biliary atresia combined with ileal atresia. Ileal resection and end to end anastomosis operation were done at second days of the life because of congenital ileal atresia. Jaundice and acholic stool were noticed a few days after the operation. He was diagnosed as biliary atresia and received Kasai operation at 23 days of the life. Therefore, we report the case with a brief review of the related literature.

저자들은 선천성 회장 폐쇄증으로 회장 절제술과 단단문합술 시행 후 황달과 무답즙성변을 보여 시행한 검사상 선천성 담도폐쇄증으로 진단받고 Kasai 술식을 시행하여 회복된 1례를 경험하였기에 보고하는 바이다.