심낭삼출을 동반한 CREST 증후군 1례

Abstract

CREST syndrome is variant of scleroderma characterized by calcinosis, Raynaud's phenomena, esophageal dysmotility, sclerodactyly & telangiectasia.

In the past, it was believed that CREST patients live longer than scleroderma because rare involvement of internal organ, but recently noted that CREST patients may die early by involvement of internal organ.

Recently， authors experience one case of CREST syndrome associated with pericardial effusion, herein presenting our experience and literature and reviewed.