계명대학교 의학도서관 Repository

소아 복벽원심성 지방위축증 1례

Metadata Downloads
Author(s)
박의수정재봉송준영
Keimyung Author(s)
Park, Eui SooSong, Joon Young
Department
Dept. of Dermatology (피부과학)
Journal Title
Keimyung Medical Journal
Issued Date
1994
Volume
13
Issue
2
Keyword
LipodystrophiaLipodystrophia centrifugalis abdominalis infantilis
Abstract
Lipodystrophia centrifugalis abdominalis infantilis(LCAI), an atypical form of progressive lipodystrophy, is a disease named by Imamura et al in 1971. The unique and distinct features of this disease are onset by age 3, development of the lesion in the groin, axillae, or their surroundings, presence of slightly inflammatory areas around the depressed one, and histologically, it shows loss of subcutaneous fat in the depressed area with panniculitis in the surrounding area. The depressed lesions are found to enlarge centrifugally for several years and to involve a large part of the abdominal and/ or chest wall. However the enlargement is found to stop spontaneously by age 13, and the depressed area tends to undergo recovery thereafter.
The patient is 9-year-old girl. She had multiple well-defined depressions of skin on abdomen, left inguinal area with deformity of labia major which was noticed 4 years prior to first diagnosis. There was no family history, no physical abnormality except skin lesion.
Complete blood cell count, urinalysis, liver function test and chest X-ray within normal limit. Biopsy specimen from surrounding erythematous area revealed slightly atrophy of the epidermis, a moderate lymphocyte infiltration around skin appendages in mid-part of dermis, decreased amount of subcutaneous adipose tissue with mild lymphocyte infiltration.
She has been treated with topical steroid. But there was no improvement of the depressed lesion except surrounding erythema.
Alternative Title
A Case of Lipodystrophia Centrifugalis Abdominalis Infantilis
Keimyung Author(s)(Kor)
박의수
송준영
Publisher
Keimyung University School of Medicine
Citation
박의수 et al. (1994). 소아 복벽원심성 지방위축증 1례. Keimyung Medical Journal, 13(2), 240–243.
Type
Article
URI
https://kumel.medlib.dsmc.or.kr/handle/2015.oak/14881
Appears in Collections:
2. Keimyung Medical Journal (계명의대 학술지) > 1994
1. School of Medicine (의과대학) > Dept. of Dermatology (피부과학)
공개 및 라이선스
  • 공개 구분공개
파일 목록

Items in Repository are protected by copyright, with all rights reserved, unless otherwise indicated.