우측 팔에 발생한 골격외 유잉육종 1례

Abstract

Extraskeletal Ewing's sarcoma is a rare primary malignant soft tissue tumor that was first described by Angervall and Enzinger in 1975. These tumors tend to occur chiefly in young adults. Because of their undifferentiated histologic appearance, the differential diagnosis must exclude other small round cell neoplasm such as neuroblastoma, rhabdomyosarcoma, neuroepithelioma, and poorly differentiated malignant lymphoma. The extraskeletal Ewing's sarcoma are mainly involved the soft tissues of the trunk and lower extremity. We recently experienced a case of extraskeletal Ewing's sarcoma of the right arm in a 53 years old male. The patient underwent local wide excision and postoperative radiation of 6.480cGy and combination chemotherapy with VP-16, adriamycin, vincristine, prednisolone and cyclophosphamide. We presented a case of extraskeletal Ewing's sarcoma in the right arm with review of world literature