외이도 진주종을 동반한 측두골에 발생한 섬유성 이형성증

Abstract

Fibrous dysplasia is a benign fibro-osseous lesion which normal osseous tissue is replaced with mixtures of fibrous tissue and mature trabecular bone. Fibrous dysplasia of temporal bone is rare, but it may lead to progressive stenosis of external auditory canal. The authors reported a case of fibrous dysplasia accompanying cholesteatoma of the external auditory canal in a 14-year-old woman. She complained about progressive hearing loss for several months. Ear examination revealed stenosis of the right external auditory canal, and in CT findings, ground-glass opacity was seen in temporal bone area. In pathologic examination, characteristic ‘Chinese letter’ pattern has been founded. She underwent right side canaloplasty via postauricular approach and meatoplasty. The patient has been followed up regularly for one year, and there is no evidence of the recurrence of the disease or associated symptoms. It is important to be aware that fibrous dysplasia of the temporal bone may accompany slowly progressive stenosis and cholesteatoma of external auditory canal and cannot be removed perfectly. So, long-term follow-up should be performed. CT examination is useful for follow-up.