다낭성낭포신 환자와 Marfan's 증후군 환자에서 발생한 뇌동맥류 -증례 보고-

Abstract

A case of an anterior communicating(Acom) artery aneurysm in a 36-year-old woman with polycystic kindey, and a case of multiple aneurysms(Acom. and anterior choroidal artery aneurysm) is a 49-year-old man with Marfan's syndrome are reported. Polycystic kidney was confirmed by abdominal ultrasonography and computed tomography. Marfan's syndrome was diagnosed with skeletal abnormalities (dolichocephaly, highly arched palate, cleft palate, arachnodactyly and tall slender height with excessive length of limbs) and marked elongation and tortuosity of the vertebral artery on cerebral angiography. Those patients were treated with the clipping of aneurysms. We will discuss the pathogenesis of cerebral aneurysm in those diseases with stress on the important points of management.