귀와 복부에 국한된 초점성 이상운동증

Abstract

Focal or segmental dystonic syndromes affecting cranial or upper limb muscles are well recognized. Restricted dystonic movements affecting axial muscle group are less common. Restricted involuntary movements of body parts such as ear and trunk which are not normally affected in isolation by movement disorders have been reported. Despite their unusual locations, the clinical and neurophysiologic characteristics of the movements were similar to dystonia and they were classified as focal dystonia. Case: We report four patients who have focal dyskinesia affecting ear and abdomen. In two patients, dyskinesia affecting the ear developed after head or facial trauma and in the other two cases, dyskinesia affecting the abdomen occurred after surgical operation. The unusual locations and appearance distinguish these dyskinesias from recognized movement disorder syndromes. The characteristic features of these dyskinesia led us to classify it as dystonia. We'd like to underline that dystonia can affect any part of the body and peripheral factors may play a role in pathogenesis of the dystonia.