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Surgical correction of total anomalous pulmonary venous return in an adult patient

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Affiliated Author(s)
장우성
Alternative Author(s)
Jang, Woo Sung
Journal Title
J Cardiothorac Surg
ISSN
1749-8090
Issued Date
2022
Keyword
Adult congenital heart surgeryComplex congenital heart diseaseTAPVRVascular anomalies
Abstract
Background:
Total anomalous pulmonary venous return (TAPVR) is rare congenital heart disease. Most TAPVRs require surgical corrections in the neonatal period and survival to adulthood without surgical correction is extremely rare. Most untreated patients with large atrial septal defects and no pulmonary venous obstruction have pulmonary vascular damage from pulmonary over circulation.

Case presentation:
44-year-old TAPVR patient admitted to our medical center. A snowman-shaped heart, including cardiomegaly and an increase in pulmonary blood flow, was seen in the chest X-ray. A large-sized (around 3 cm) atrial septal defect with dilated right atrium, right ventricle, and pulmonary artery was detected on echocardiography. Heart computed tomography was performed for further evaluation, and supra-cardiac type TAPVR without any obstructive lesion was identified.

Conclusions:
TAPVR in an adult patient is extremely rare, and this patient was treated successfully with surgical correction and is doing well. A sinus rhythm and mild mitral valve regurgitation have remained during 2.5 years of outpatient follow-up.
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