소아 복벽원심성 지방위축증 1례

Other Titles
A Case of Lipodystrophia Centrifugalis Abdominalis Infantilis
Authors
박의수정재봉송준영
Department
Dept. of Dermatology (피부과학)
Issue Date
1994
Citation
Keimyung Medical Journal, Vol.13(2) : 240-243, 1994
Abstract
Lipodystrophia centrifugalis abdominalis infantilis(LCAI), an atypical form of progressive lipodystrophy, is a disease named by Imamura et al in 1971. The unique and distinct features of this disease are onset by age 3, development of the lesion in the groin, axillae, or their surroundings, presence of slightly inflammatory areas around the depressed one, and histologically, it shows loss of subcutaneous fat in the depressed area with panniculitis in the surrounding area. The depressed lesions are found to enlarge centrifugally for several years and to involve a large part of the abdominal and/ or chest wall. However the enlargement is found to stop spontaneously by age 13, and the depressed area tends to undergo recovery thereafter. The patient is 9-year-old girl. She had multiple well-defined depressions of skin on abdomen, left inguinal area with deformity of labia major which was noticed 4 years prior to first diagnosis. There was no family history, no physical abnormality except skin lesion. Complete blood cell count, urinalysis, liver function test and chest X-ray within normal limit. Biopsy specimen from surrounding erythematous area revealed slightly atrophy of the epidermis, a moderate lymphocyte infiltration around skin appendages in mid-part of dermis, decreased amount of subcutaneous adipose tissue with mild lymphocyte infiltration. She has been treated with topical steroid. But there was no improvement of the depressed lesion except surrounding erythema.
Keywords
LipodystrophiaLipodystrophia centrifugalis abdominalis infantilis
URI
http://kumel.medlib.dsmc.or.kr/handle/2015.oak/14881
Appears in Collections:
1. Journal Papers (연구논문) > 1. School of Medicine (의과대학) > Dept. of Dermatology (피부과학)
2. Keimyung Medical Journal (계명의대 학술지) > 1994
Keimyung Author(s)
박의수; 송준영
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